This Article Full Text (PDF) References Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Alert me to new issues of the journal Add to Saved Citations Download to citation manager Request Permissions Request Reprints Add to My Marked Citations Citing Articles Citing Articles via Google Scholar Citing Articles via Scopus Google Scholar Articles by Stella, A. Articles by Guizzardi, S. Search for Related Content PubMed Articles by Stella, A. Articles by Guizzardi, S. Social Bookmarking                         What's this?

Sack-Barabas Syndrome (Ehlers-Danlos IV Type) (Clinic and Histopathologic Ultrastructural Correlations)

Department of Surgery, Chair of Vascular Surgery, University of Bologna, Bologna, Italy

M. Gessaroli

Department of Surgery, Chair of Vascular Surgery, University of Bologna, Bologna, Italy

B.I. Cifiello

Department of Surgery, Chair of Vascular Surgery, University of Bologna, Bologna, Italy

M. Mirelli

Department of Surgery, Chair of Vascular Surgery, University of Bologna, Bologna, Italy

V. Loperfido

Department of Surgery, Chair of Vascular Surgery, University of Bologna, Bologna, Italy

R. Riva

From the Institute of Normal Human Anatomy, University of Bologna, Bologna, Italy

S. Guizzardi

From the Institute of Normal Human Anatomy, University of Bologna, Bologna, Italy

The patient that led the authors to make some physiopathological reflections on the Ehlers-Danlos syndrome (EDS) was a young 30 year old suffering from a poly-aneurismatic syndrome, identifiable as EDS type IV.

After a surgical treatment on the abdominal aortic aneurysm and an aorto bis-iliac by-pass, a specimen of the aortic wall was the subject of an ultrastruc tural study.

In particular, correlations between the histopathological alterations were sought.

Particular reference was made to the collagen and the clinical vascular mani festations found not only in this patient but also repeatedly in other patients suffering from this type of EDS.

Vascular and Endovascular Surgery, Vol. 20, No. 2, 67-73 (1986)
DOI: 10.1177/153857448602000201


CiteULike    Complore    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter    What's this?